In:
Advances in Respiratory Medicine, MDPI AG, Vol. 86, No. 5 ( 2018-10-30), p. 249-254
Abstract:
Pulmonary veno-occlusive disease (PVOD) is a rare form of pulmonary hypertension caused by alteration of pulmonary veins. Many clinical and hemodynamic similarities to idiopathic pulmonary arterial hypertension (IPAH) may cause diagnostic and therapeutic difficulties. This case report is about a patient with PVOD, whose first symptoms of the disease occurred after infectious mononucleosis. The patient was administered prostacycline (PGI2) mimetic (Treprostinil), which made qualification process and lung transplantation possible. Despite more and more knowledge about the causes, ethiopathogenesis and changes in pulmonary veins on molecular level, lung transplantation is the only successful therapeutic option for patients suffering from PVOD.
Type of Medium:
Online Resource
ISSN:
2543-6031
DOI:
10.5603/ARM.2018.0040
Language:
English
Publisher:
MDPI AG
Publication Date:
2018
detail.hit.zdb_id:
2893877-X
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