In:
Neurology, Ovid Technologies (Wolters Kluwer Health), Vol. 99, No. 15 ( 2022-10-11), p. 660-664
Kurzfassung:
Encephalitis and encephalopathy in children represent a diagnostic challenge. We describe a patient with relapsing encephalitis in whom the differential diagnosis included acute disseminated encephalomyelitis, human herpesvirus 6 encephalitis, and hemophagocytic lymphohistiocytosis (HLH). Because of its rarity, HLH is often overlooked as a differential diagnosis in encephalitis, especially in the isolated CNS forms. As this case illustrates, inborn errors of immunity can underlie isolated encephalitis and should be included in the differential diagnosis of these presentations.
Materialart:
Online-Ressource
ISSN:
0028-3878
,
1526-632X
DOI:
10.1212/WNL.0000000000201124
Sprache:
Englisch
Verlag:
Ovid Technologies (Wolters Kluwer Health)
Publikationsdatum:
2022
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