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Management of lower limb deformities in children with osteogenesis imperfecta

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Abstract

Osteogenesis imperfecta (OI) often leads to severe lower limb (LL) deformities due to recurrent fractures that significantly hamper ambulation. We describe our management experience of correction of LL deformities in four children with OI. Medical management consisted of peri and postoperative pamidronate therapy, calcium supplementation and rehabilitative care. Deformities were corrected with multiple osteotomies and intramedullary fixation by titanium elastic nails. At a mean follow-up of 30 months, all children have significantly reduced fracture incidence and have no evidence of recurrence of deformities with improved ambulatory status. We emphasize the importance of combined medical and surgical therapy for these patients.

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Authors and Affiliations

  1. Department of Pediatrics, Apollo Center for Advanced Pediatrics, Indraprastha Apollo Hospital, New Delhi, India

    Satvinder Kaur & Ketan Prasad Kulkarni

  2. Department of Pediatric Endocrinology, Apollo Center for Advanced Pediatrics, Indraprastha Apollo Hospital, New Delhi, India

    Inderpal Singh Kochar

  3. Department of Pediatric Orthopedics, Apollo Center for Advanced Pediatrics, Indraprastha Apollo Hospital, New Delhi, India

    Ramani Narasimhan

Authors
  1. Satvinder Kaur
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  2. Ketan Prasad Kulkarni
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  3. Inderpal Singh Kochar
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  4. Ramani Narasimhan
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Correspondence to Inderpal Singh Kochar.

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Kaur, S., Kulkarni, K.P., Kochar, I.S. et al. Management of lower limb deformities in children with osteogenesis imperfecta. Indian Pediatr 48, 637–639 (2011). https://doi.org/10.1007/s13312-011-0103-0

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  • DOI: https://doi.org/10.1007/s13312-011-0103-0

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