Abstract
Primary cardiac liposarcomas are extremely rare. We present an extremely rare case of primary cardiac liposarcoma in the right ventricular outflow tract, tethered to the pulmonary valve and prolapsing in the pulmonary artery during systole in a young symptomatic male patient. Complete excision of the liposarcoma with the pulmonary valve cusp and reconstruction of the pulmonary valve were performed.
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Video 1
Cardiac cine MRI showing a well-defined pedunculated T2 hypointense variegated mass arising from the posterolateral wall of the right ventricular outflow tract, tethered to the pulmonary valve and oscillating with the pulmonary valve in systole and diastole. (MP4 740 kb)
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Parashi, H.S., Joshi, M.M., Bhosle, K.N. et al. Primary cardiac liposarcoma in the right ventricular outflow tract. Indian J Thorac Cardiovasc Surg 33, 332–335 (2017). https://doi.org/10.1007/s12055-017-0543-9
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DOI: https://doi.org/10.1007/s12055-017-0543-9