In:
Cardiology in the Young, Cambridge University Press (CUP), Vol. 2, No. 2 ( 1992-04), p. 196-199
Abstract:
We studied the cardiac conduction system in a case of Hurler syndrome. There was dense fibrosis of the supporting matrix of the sinus node and accumulation of mucopolysaccharide in the nodal cells. The bundle branches showed prominent hydropic degeneration, being encased and punctuated by dense fibrous tissue. These changes in the conduction system may predispose to the development of arrhythmias, accounting for the sudden deaths in Hurler syndrome.
Type of Medium:
Online Resource
ISSN:
1047-9511
,
1467-1107
DOI:
10.1017/S1047951100000858
Language:
English
Publisher:
Cambridge University Press (CUP)
Publication Date:
1992
detail.hit.zdb_id:
2060876-7