In:
Pediatric Transplantation, Wiley, Vol. 20, No. 2 ( 2016-03), p. 271-275
Kurzfassung:
The clinical outcome of allogeneic HSCT was retrospectively analyzed in eight patients with CHS . In total, six of these eight patients are alive. Four of five patients transplanted with MAC achieved prompt engraftment, and three of the four patients, including two patients with AP before transplant, are alive without disease. In contrast, three patients transplanted with RIC without active AP disease achieved prompt engraftment and survive long term. RIC ‐ HSCT might be an alternative treatment for CHS similar to other types of HLH, at least for patients without active AP disease.
Materialart:
Online-Ressource
ISSN:
1397-3142
,
1399-3046
DOI:
10.1111/petr.2016.20.issue-2
Sprache:
Englisch
Verlag:
Wiley
Publikationsdatum:
2016
ZDB Id:
2008614-3